Lipoma of Columella with septal extension in Pai syndrome: report of a rare case
نویسندگان
چکیده
BACKGROUND Lipoma in nasal region in a case of Pai syndrome is very rare. Very few cases of Pai syndrome with columellar lipoma with extension to septum and tip have been reported till date. CASE PRESENTATION We report a very rare form of nasal lipoma in a case of Pai syndrome with extension to septum and tip in a 4 year old female child. CONCLUSIONS Pai syndrome with columellar lipoma with septal and tip extension should always be kept in mind when evaluating a swelling in the region of nasal tip, collumella and septum with notch in upper lip and corpus callosal lipoma.
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